TY - JOUR T1 - Adherence to guidelines in idiopathic pulmonary fibrosis: a follow-up national survey JF - ERJ Open Research JO - erjor DO - 10.1183/23120541.00032-2015 VL - 1 IS - 2 SP - 00032-2015 AU - Vincent Cottin AU - Emmanuel Bergot AU - Arnaud Bourdin AU - Jacques Cadranel AU - Philippe Camus AU - Bruno Crestani AU - Jean-Charles Dalphin AU - Philippe Delaval AU - Claire Dromer AU - Dominique Israel-Biet AU - Romain Kessler AU - Sylvain Marchand-Adam AU - Charles Hugo Marquette AU - Grégoire Prévot AU - Martine Reynaud-Gaubert AU - Dominique Valeyre AU - Benoit Wallaert AU - Benoit Bouquillon AU - Jean-François Cordier Y1 - 2015/10/01 UR - http://openres.ersjournals.com/content/1/2/00032-2015.abstract N2 - A new survey coordinated by the French expert centres for rare pulmonary diseases investigated French pulmonologists' diagnostic and therapeutic practice for idiopathic pulmonary fibrosis (IPF) and explored changes since a previous survey in 2011–2012.From May 16 to August 30, 2014, 524 pulmonologists were contacted. Those following at least one patient with IPF were invited to complete a questionnaire administered by telephone or e-mail.166 (31.7%) pulmonologists, 161 (97%) of whom had participated to the first survey, completed the questionnaire. Of those, 46% and 52%, respectively, discussed the cases with radiologists and pathologists. Out of 144 pulmonologists practicing outside of expert centres, 80% indicated referring patients to those centres. The 2013 French practical guidelines for IPF were known by 92% of pulmonologists involved in IPF, 96% of whom considered them appropriate for practice. The multidisciplinary discussion form for IPF diagnosis was known by 74% and considered appropriate by 94%. Diagnosis and management resulted from multidisciplinary discussion in 50% of the cases. About 58% of patients were diagnosed with “mild to moderate IPF” as defined by forced vital capacity ≥50% of the predicted value and diffusing capacity for carbon monoxide ≥35% of predicted. At the time of the survey, 31% of physicians were using pirfenidone to treat patients with “mild-to-moderately severe IPF” and 30% generally prescribed no treatment.Substantial improvement has occurred since the 2011–2012 survey with regard to knowledge of guidelines and proper management of IPF. Early diagnosis still needs to be improved through the network of expert centres.A practice survey reveals important changes in the diagnosis and practical management of IPF http://ow.ly/Tuwr1 ER -