TABLE 1

Demographics of the study subjects

HealthyCFPCD
Subjects n202017
 Males989
Age years13.3±1.899.9±3.6111.8±3.76
Weight kg48.1±12.5131.7±12.8945.5±15.1
Weight z-score#0.05±0.90−0.33±0.790.62±1.22
Height cm157.9±11.76134.4±19.35147.2±19.37
Height z-score#0.19±1.06−0.33±0.950.12±1.15
LCIstandard7.10±0.5610.13±2.00¶,+10.12±2.21¶,+

Data are presented as mean±sd, unless otherwise stated. CF: cystic fibrosis; PCD: primary ciliary dyskinesia; LCIstandard: lung clearance index calculated according to the current recommendations [9]. #: z-scores calculated according to Centers for Disease Control and Prevention growth charts [30]; : p<0.001, unpaired t-test, compared with healthy subjects; +: p=0.3, unpaired t-test between CF and PCD groups.