Background IgG4-sclerosing cholangitis (IgG4-SC) patients have an increased level of serum
IgG4, dense infiltration of IgG4-positive plasma cells with extensive fibrosis in the bile duct …

Background Sclerosing pancreatitis is a unique form of pancreatitis that is characterized by
irregular narrowing of the main pancreatic duct, lymphoplasmacytic inflammation of the …

… Kubota T, Moritani S, Yoshino T, Nagai H, Terasaki H. Ocular adnexal marginal zone B cell
… Masaki Y, Sugai S, Umehara H. IgG4-related diseases including Mikulicz’s disease and …

Objective: To establish an appropriate steroid treatment regimen for autoimmune pancreatitis
(AIP). Methods: A retrospective survey of AIP treatment was conducted in 17 centres in …

… Uehara T, Hamano H, Kawa S, Sano K, Honda T, Ota H. Distinct clinicopathological
entity ‘autoimmune pancreatitis-associated sclerosing cholangitis’. Pathol Int 2005;55:405–11. …

Mitochondrial neurogastrointestinal encephalomyopathy (MNGIE) is an autosomal
recessive disorder defined clinically by severe gastrointestinal dysmotility; cachexia; ptosis, …

BACKGROUND & AIMS: Autoimmune pancreatitis is a distinctive disease entity characterized
by high serum immunoglobulin G4 concentrations. Because of the close association …

… Pancreatograms in the left column (A, C, E, G) were obtained before corticosteroid therapy;
those in the right column (B, D, F, H) … H, Pancreatogram in same patient as G after treatment. …

Autoimmune pancreatitis (AIP) is characterized by high serum immunoglobin (Ig) G4
concentrations, lymphoplasmacytic inflammation, and a favorable response to corticosteroid …

Objective Corticosteroid has been established as the standard therapy for autoimmune
pancreatitis (AIP), but the requirement for maintenance corticosteroid therapy is controversial. We …