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CF and non-CF bronchiectasis

  • Urinary bicarbonate and metabolic alkalosis during exacerbations in cystic fibrosis
    Giulia Spoletini, Giles Fitch, Lindsey Gillgrass, Christine Etherington, Ian Clifton, Daniel G. Peckham
    ERJ Open Research Apr 2022, 8 (2) 00669-2021; DOI: 10.1183/23120541.00669-2021
  • Chronic cough in cystic fibrosis: the effect of modulator therapy on objective 24-h cough monitoring
    Mengru Zhang, Kayleigh Brindle, Melanie Robinson, Debbie Ingram, Tanya Cavany, Alyn Morice
    ERJ Open Research Apr 2022, 8 (2) 00031-2022; DOI: 10.1183/23120541.00031-2022
  • Novel CFTR modulator combinations maximise rescue of G85E and N1303K in rectal organoids
    Marjolein M. Ensinck, Liesbeth De Keersmaecker, Anabela S. Ramalho, Senne Cuyx, Stephanie Van Biervliet, Lieven Dupont, Frauke Christ, Zeger Debyser, François Vermeulen, Marianne S. Carlon
    ERJ Open Research Apr 2022, 8 (2) 00716-2021; DOI: 10.1183/23120541.00716-2021
  • An observational study of Pseudomonas aeruginosa in adult long-term ventilation
    Ruth Sobala, Hannah Carlin, Thomas Fretwell, Sufyan Shakir, Katie Cattermole, Amy Royston, Paul McCallion, John Davison, Joanna Lumb, Hilary Tedd, Ben Messer, Anthony De Soyza
    ERJ Open Research Apr 2022, 8 (2) 00687-2021; DOI: 10.1183/23120541.00687-2021
  • CFTR modulator use and risk of nontuberculous mycobacteria positivity in cystic fibrosis, 2011–2018
    Emily E. Ricotta, D. Rebecca Prevots, Kenneth N. Olivier
    ERJ Open Research Apr 2022, 8 (2) 00724-2021; DOI: 10.1183/23120541.00724-2021
  • Respiratory symptoms of Swiss people with primary ciliary dyskinesia
    Myrofora Goutaki, Leonie Hüsler, Yin Ting Lam, Helena M. Koppe, Andreas Jung, Romain Lazor, Loretta Müller, Swiss PCD Research Group, Eva S.L. Pedersen, Claudia E. Kuehni
    ERJ Open Research Apr 2022, 8 (2) 00673-2021; DOI: 10.1183/23120541.00673-2021
  • Research advances and clinical management of bronchiectasis: Chinese perspective
    Jin-fu Xu, Yong-hua Gao, Yuan-lin Song, Jie-ming Qu, Wei-jie Guan
    ERJ Open Research Apr 2022, 8 (2) 00017-2022; DOI: 10.1183/23120541.00017-2022
  • Curvilinearity provides additional information to lung clearance index only in a minority of children with early cystic fibrosis lung disease
    Samantha Irving, Katie Bayfield, Jane C. Davies, Andrew Bush
    ERJ Open Research Apr 2022, 8 (2) 00582-2021; DOI: 10.1183/23120541.00582-2021
  • An international survey on nasal nitric oxide measurement practices for the diagnosis of primary ciliary dyskinesia
    Nicole Beydon, Thomas Ferkol, Amanda Lea Harris, Murielle Colas, Stephanie D. Davis, Eric Haarman, Claire Hogg, Emma Kilbride, Panayotis Kouis, Claudia E. Kuehni, Philipp Latzin, Diana Marangu, June Marthin, Kim G. Nielsen, Phil Robinson, Nisreen Rumman, Matthew Rutter, Woolf Walker, Jane S. Lucas
    ERJ Open Research Apr 2022, 8 (2) 00708-2021; DOI: 10.1183/23120541.00708-2021
  • Comparison of different sets of immunological tests to identify treatable immunodeficiencies in adult bronchiectasis patients
    Stefano Aliberti, Francesco Amati, Andrea Gramegna, Barbara Vigone, Martina Oriano, Giovanni Sotgiu, Marco Mantero, Edoardo Simonetta, Laura Saderi, Anna Stainer, Serena Tammaro, Paola Marchisio, Eva Polverino, James D. Chalmers, Francesco Blasi
    ERJ Open Research Jan 2022, 8 (1) 00388-2021; DOI: 10.1183/23120541.00388-2021

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  • The safety of cardioselective β1-blockers in asthma: literature review and search of global pharmacovigilance safety reports
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