Patient characteristics | |
Mean age (range) | 49 (22-83) yrs |
Sex (male) | 62% |
Long term care facility residents | 31% |
Diagnosis | |
- Congenital muscular dystrophy | 38% |
- Multiple sclerosis | 20% |
- Other | 42% |
Non-invasive ventilation | 62% |
Bulbar involvement | 58% |
Cough peak flow (mean±SD) | 126.2±69 L/min |