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More articles from Cystic fibrosis

  • Magnetic resonance imaging detects onset and association with lung disease severity of bronchial artery dilatation in cystic fibrosis
    Patricia Leutz-Schmidt, Daiva-Elzbieta Optazaite, Olaf Sommerburg, Monika Eichinger, Sabine Wege, Eva Steinke, Simon Y. Graeber, Michael U. Puderbach, Jens-Peter Schenk, Abdulsattar Alrajab, Simon M.F. Triphan, Hans-Ulrich Kauczor, Mirjam Stahl, Marcus A. Mall, Mark O. Wielpütz
    ERJ Open Research Mar 2023, 9 (2) 00473-2022; DOI: 10.1183/23120541.00473-2022
  • High-throughput functional assay in cystic fibrosis patient-derived organoids allows drug repurposing
    Sacha Spelier, Eyleen de Poel, Georgia N. Ithakisiou, Sylvia W.F. Suen, Marne C. Hagemeijer, Danya Muilwijk, Annelotte M. Vonk, Jesse E. Brunsveld, Evelien Kruisselbrink, Cornelis K. van der Ent, Jeffrey M. Beekman
    ERJ Open Research Jan 2023, 9 (1) 00495-2022; DOI: 10.1183/23120541.00495-2022
  • Nasal epithelial cell culture fluorescence recovery after photobleaching predicts cystic fibrosis therapeutic response
    Timothy E. Corcoran, Carol A. Bertrand, Michael M. Myerburg, Daniel J. Weiner, Sheila A. Frizzell, Anna Li, Brittani Agostini, Robert S. Parker, Monica E. Shapiro, Ashok Muthukrishnan, Nicholas D. Hages, Brian P. Mulhern, Joseph M. Pilewski
    ERJ Open Research Oct 2022, 8 (4) 00382-2022; DOI: 10.1183/23120541.00382-2022
  • Diagnostic agreement among experts assessing adults presenting with possible cystic fibrosis: need for improvement and implications for patient care
    Alessandro N. Franciosi, April Tanzler, Jodi Goodwin, Pearce G. Wilcox, George M. Solomon, Albert Faro, Noel G. McElvaney, Damian G. Downey, Bradley S. Quon
    ERJ Open Research Oct 2022, 8 (4) 00227-2022; DOI: 10.1183/23120541.00227-2022
  • Long-term effectiveness of dual CFTR modulator treatment of cystic fibrosis
    Danya Muilwijk, Domenique D. Zomer-van Ommen, Vincent A.M. Gulmans, Marinus J.C. Eijkemans, Cornelis K. van der Ent, Dutch Cystic Fibrosis Registry (NCFR) Steering Group: , J. Altenburg, S.W.J. Terheggen-Lagro, H.G.M. Heijerman, K.M. de Winter-de Groot, M. Bakker, R.A.S. Hoek, H.M. Janssens, R. van der Meer, M. Nuijsink, H. van der Vaart, G.H. Koppelman, L.H. Conemans, M.A.G.E. Bannier, J.J. Noordhoek
    ERJ Open Research Oct 2022, 8 (4) 00204-2022; DOI: 10.1183/23120541.00204-2022
  • The long-term effects of insulin use in incident cystic fibrosis-related diabetes: a target trial emulated using longitudinal national registry data
    Emily Granger, Ruth H. Keogh, Freddy Frost
    ERJ Open Research Oct 2022, 8 (4) 00170-2022; DOI: 10.1183/23120541.00170-2022
  • Novel CFTR modulator combinations maximise rescue of G85E and N1303K in rectal organoids
    Marjolein M. Ensinck, Liesbeth De Keersmaecker, Anabela S. Ramalho, Senne Cuyx, Stephanie Van Biervliet, Lieven Dupont, Frauke Christ, Zeger Debyser, François Vermeulen, Marianne S. Carlon
    ERJ Open Research Apr 2022, 8 (2) 00716-2021; DOI: 10.1183/23120541.00716-2021
  • CFTR modulator use and risk of nontuberculous mycobacteria positivity in cystic fibrosis, 2011–2018
    Emily E. Ricotta, D. Rebecca Prevots, Kenneth N. Olivier
    ERJ Open Research Apr 2022, 8 (2) 00724-2021; DOI: 10.1183/23120541.00724-2021
  • Novel volumetric capnography indices measure ventilation inhomogeneity in cystic fibrosis
    Sotirios Fouzas, Anne-Christianne Kentgens, Olga Lagiou, Bettina Sarah Frauchiger, Florian Wyler, Ilias Theodorakopoulos, Sophie Yammine, Philipp Latzin
    ERJ Open Research Jan 2022, 8 (1) 00440-2021; DOI: 10.1183/23120541.00440-2021
  • Cross-talk of inflammatory mediators and airway epithelium reveals the cystic fibrosis transmembrane conductance regulator as a major target
    Filipa B. Simões, Arthur Kmit, Margarida D. Amaral
    ERJ Open Research Oct 2021, 7 (4) 00247-2021; DOI: 10.1183/23120541.00247-2021

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