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History
- Received June 21, 2021
- Accepted September 12, 2021
- Published online October 28, 2021.
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Author Information
- Andreas Jung1,48⇑,
- Annalisa Orenti2,48,
- Fiona Dunlevy3,48,
- Elina Aleksejeva4,
- Egil Bakkeheim5,
- Vladimir Bobrovnichy6,
- Siobhán B. Carr7,
- Carla Colombo8,
- Harriet Corvol9,
- Rebecca Cosgriff10,
- Géraldine Daneau11,
- Deniz Dogru12,
- Pavel Drevinek13,
- Andrea Dugac Vukic14,
- Isabelle Fajac15,16,
- Alice Fox3,
- Stojka Fustik17,
- Vincent Gulmans18,
- Satenik Harutyunyan19,
- Elpis Hatziagorou20,
- Irena Kasmi21,
- Hana Kayserová22,
- Elena Kondratyeva23,
- Uroš Krivec24,
- Halyna Makukh25,
- Kestutis Malakauskas26,
- Edward F. McKone27,
- Meir Mei-Zahav28,29,
- Isabelle de Monestrol30,
- Hanne Vebert Olesen31,
- Rita Padoan32,33,
- Tsitsino Parulava34,
- Maria Dolores Pastor-Vivero35,
- Luísa Pereira36,
- Guergana Petrova37,
- Andreas Pfleger38,
- Liviu Pop39,
- Jacqui G. van Rens3,
- Milan Rodić40,
- Marc Schlesser41,
- Valérie Storms42,
- Oxana Turcu43,
- Lukasz Woźniacki44,
- Panayiotis Yiallouros45,
- Anna Zolin2,
- Damian G. Downey46,49 and
- Lutz Naehrlich47,49
- 1Paediatric Pulmonology, University Children's Hospital Zurich, Zurich, Switzerland
- 2Department of Clinical Sciences and Community Health, Laboratory of Medical Statistics, Epidemiology and Biometry G. A. Maccacaro, University of Milan, Milan, Italy
- 3European Cystic Fibrosis Society, Karup, Denmark
- 4Department of Pneumology, Children's Clinical University Hospital, Rīga Stradinš University, Riga, Latvia
- 5Dep. of Paediatrics, Norwegian Cystic Fibrosis Registry, Oslo University Hospital, Oslo, Norway
- 6Belarusian Republic Children's Center of Pulmonology and Cystic Fibrosis, Pulmonary Department, 3rd City Children's Clinical Hospital, Minsk, Belarus
- 7Department of Respiratory Paediatrics, Royal Brompton Hospital; NHLI, Imperial College, London, UK
- 8Department of Pathophysiology and Transplantation, Cystic Fibrosis Reference Center of Lombardia Region, Fondazione IRCCS Ca' Granda Ospedale Maggiore Policlinico, University of Milan, Milan, Italy
- 9Pediatric Pulmonology Department and Cystic Fibrosis Center, Sorbonne Université, Centre de Recherche Saint-Antoine, Inserm UMR_S938, Assistance Publique-Hôpitaux de Paris, Hôpital Trousseau, Paris, France
- 10Cystic Fibrosis Trust, London, UK
- 11Sciensano, Epidemiology and public health, Health services research, Brussels, Belgium
- 12Cystic Fibrosis Registry of Turkey, Ankara, Turkey
- 13Department of Medical Microbiology, Second Faculty of Medicine, Charles University and Motol University Hospital, Prague, Czech Republic
- 14University Hospital Centre Zagreb, Cystic Fibrosis Centre - Paediatrics and Adults, Zagreb, Croatia
- 15Université Paris Descartes, Sorbonne Paris Cité, Paris, France
- 1616AP-HP, Hôpital Cochin, Service de Physiologie et Explorations Fonctionnelles, Paris, France
- 17Centre for Cystic Fibrosis, University Children's Hospital, Skopje, North Macedonia
- 18Dutch Cystic Fibrosis Foundation (NCFS), Baarn, The Netherlands
- 19Yerevan University CF Centre, Muratsan Hospital, Yerevan, Armenia
- 20Cystic Fibrosis Unit, Hippokration General Hospital, Aristotle University of Thessaloniki, Thessaloniki, Greece
- 21Department of Paediatrics, “Mother Thereza” Hospital Center, Tirana, Albania
- 22Cystic Fibrosis Centre, University Hospital of Bratislava, Bratislava, Slovakia
- 23Clinical research department of cystic fibrosis “Research Centre for Medical Genetics”, Moscow, Russian Federation
- 24Department of Paediatric Pulmonology, University Children's Hospital, Ljubljana University Medical Centre, Ljubljana, Slovenia
- 25Institute of Hereditary Pathology Ukrainian National Academy of Medical Sciences, Lviv, Ukraine
- 26Adult Cystic Fibrosis center, Department of Pulmonology, Lithuanian University of Health Sciences, Kaunas, Lithuania
- 27St. Vincent's University Hospital & University College Dublin School of Medicine, Dublin, Ireland
- 28Pulmonary Institute, Schneider Children's Medical Center of Israel, Petah Tikva, Israel
- 29Sackler Faculty of Medicine, Tel Aviv University, Tel Aviv, Israel
- 30Stockholm CF centre, Karolinska University Hospital, Karolinska Institutet, Stockholm, Sweden
- 31Department of Pediatrics and Adolescent Medicine, Cystic Fibrosis Center, Aarhus University Hospital, Aarhus, Denmark
- 32Department of Paediatrics, Cystic Fibrosis Regional Support Centre, University of Brescia, Brescia
- 33Scientific Board of Italian CF Registry, Rome, Italy
- 34I. Tsitsishvili Children's Clinic, CF Centre, Tblisi, Georgia
- 35Pediatric Pneumology and Cystic Fibrosis Unit, Osakidetza, Hospital Universitario Cruces, Bizkaia, Spain
- 36Centre for Cystic Fibrosis, Hospital de Santa Maria, Lisbon, Portugal
- 37Pediatric Clinic, Alexandrovska University Hospital, Medical University, Sofia, Bulgaria
- 38Department of Pediatrics and Adolescent Medicine, Division of Pediatric Pulmonology and Allergology, Medical University of Graz, Graz, Austria
- 39Victor Babes University of Medicine and Pharmacy Timisoara, National Cystic Fibrosis Centre Timisoara, Romania
- 40National Centre for Cystic Fibrosis, Mother and Child Health Institute of Serbia “Dr Vukan Čupić”, Belgrade, Serbia
- 41Department of Pulmonology, Hôpital Robert Schuman, Luxembourg, Luxembourg
- 42Cystic Fibrosis Europe, Brussels, Belgium
- 43Department of Pediatrics, Ambulatory Cystic Fibrosis and Other Rare Diseases Center, Institute for Maternal and Child Healthcare, State University of Medicine and Pharmacy “Nicolae Testemitanu”, Chisinau, Republic of Moldova
- 44Dziekanow Paediatric Hospital, Cystic Fibrosis Centre, Institute of Mother and Child, Warsaw, Poland
- 45Medical School, University of Cyprus, Nicosia, Cyprus
- 46Wellcome-Wolfson Institute for Experimental Medicine, Queen's University Belfast; Regional Respiratory Centre Belfast City Hospital, Belfast, Northern Ireland
- 47Universities of Giessen and Marburg Lung Center, German Center of Lung Research, Justus-Liebig-University Giessen, Giessen, Germany
- 48Contributed equally as first author
- 49Contributed equally as last author
- Andreas Jung (Andreas.Jung{at}kispi.uzh.ch)
Funding
Chiesi Farmaceutici
CHF-SPONS-00147