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Demographic and clinical characteristics of patients with alpha-1 antitrypsin deficiency genotypes PI*ZZ and PI*SZ in the Spanish registry of EARCO

María Torres-Durán, José Luis López-Campos, Juan Luis Rodríguez-Hermosa, Cristina Esquinas, Cristina Martínez-González, José María Hernández-Pérez, Carlota Rodríguez, Ana Bustamante, Francisco Casas-Maldonado, Miriam Barrecheguren, Cruz González, Marc Miravitlles
ERJ Open Research 2022; DOI: 10.1183/23120541.00213-2022
María Torres-Durán
1Servicio de Neumología, Hospital Álvaro Cunqueiro, NeumoVigo I+i Research Group, IIS Galicia Sur, Vigo, Spain
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José Luis López-Campos
2Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), Instituto de Salud Carlos III, Madrid, Spain
3Unidad Médico-Quirúrgica de Enfermedades Respiratorias, Instituto de Biomedicina de Sevilla (IBiS), Hospital Universitario Virgen del Rocío/Universidad de Sevilla, Sevilla, Spain
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  • ORCID record for José Luis López-Campos
Juan Luis Rodríguez-Hermosa
4Servicio de Neumología, Hospital Clínico de San Carlos, Departamento de Medicina, Facultad de Medicina, Universidad Complutense de Madrid, Madrid, Spain
5Research Institute of Hospital Clínico San Carlos (IdISSC), Madrid, Spain
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Cristina Esquinas
2Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), Instituto de Salud Carlos III, Madrid, Spain
6Pneumology Department, Hospital Universitari Vall d'Hebron; Vall d'Hebron Institut de Recerca (VHIR), Vall d'Hebron Barcelona Hospital Campus, Barcelona, Spain
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Cristina Martínez-González
7Pneumology Department, Hospital Universitario Central de Asturias, Instituto de Investigacion Sanitaria del Principado de Asturias, Oviedo, Spain
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  • ORCID record for Cristina Martínez-González
José María Hernández-Pérez
8Pneumology Department, Hospital Universitario Nuestra Señora de La Candelaria, Santa Cruz de Tenerife, Spain
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  • ORCID record for José María Hernández-Pérez
Carlota Rodríguez
9Servicio de Neumología, Complejo Hospitalario Clínico-Universitario de Santiago, Santiago de Compostela, Spain
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Ana Bustamante
10Pneumology Section, Hospital Sierrallana-TresMares, Cantabria, Spain
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Francisco Casas-Maldonado
11Servicio de Neumología, Hospital Clínico Universitario San Cecilio. Departamento de Medicina, Facultad de Medicina, Universidad de Granada, Granada, Spain
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Miriam Barrecheguren
2Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), Instituto de Salud Carlos III, Madrid, Spain
6Pneumology Department, Hospital Universitari Vall d'Hebron; Vall d'Hebron Institut de Recerca (VHIR), Vall d'Hebron Barcelona Hospital Campus, Barcelona, Spain
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Cruz González
12Servicio de Neumología, Hospital Clínico Universitario, Instituto de Investigación INCLIVA, Valencia, Spain
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Marc Miravitlles
2Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), Instituto de Salud Carlos III, Madrid, Spain
6Pneumology Department, Hospital Universitari Vall d'Hebron; Vall d'Hebron Institut de Recerca (VHIR), Vall d'Hebron Barcelona Hospital Campus, Barcelona, Spain
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  • For correspondence: marcm@separ.es
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Article Information

DOI 
https://doi.org/10.1183/23120541.00213-2022

Published By 
European Respiratory Society
Online ISSN 
2312-0541
History 
  • Received May 2, 2022
  • Accepted May 26, 2022
  • Published online June 23, 2022.

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  • You are currently viewing a previous version of this article (June 23, 2022 - 06:43).
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Copyright ©The authors 2022 This version is distributed under the terms of the Creative Commons Attribution Non-Commercial Licence 4.0. For commercial reproduction rights and permissions contact permissions@ersnet.org

Author Information

  1. María Torres-Durán1,
  2. José Luis López-Campos2,3,
  3. Juan Luis Rodríguez-Hermosa4,5,
  4. Cristina Esquinas2,6,
  5. Cristina Martínez-González7,
  6. José María Hernández-Pérez8,
  7. Carlota Rodríguez9,
  8. Ana Bustamante10,
  9. Francisco Casas-Maldonado11,
  10. Miriam Barrecheguren2,6,
  11. Cruz González12 and
  12. Marc Miravitlles2,6⇑
  1. 1Servicio de Neumología, Hospital Álvaro Cunqueiro, NeumoVigo I+i Research Group, IIS Galicia Sur, Vigo, Spain
  2. 2Centro de Investigación Biomédica en Red de Enfermedades Respiratorias (CIBERES), Instituto de Salud Carlos III, Madrid, Spain
  3. 3Unidad Médico-Quirúrgica de Enfermedades Respiratorias, Instituto de Biomedicina de Sevilla (IBiS), Hospital Universitario Virgen del Rocío/Universidad de Sevilla, Sevilla, Spain
  4. 4Servicio de Neumología, Hospital Clínico de San Carlos, Departamento de Medicina, Facultad de Medicina, Universidad Complutense de Madrid, Madrid, Spain
  5. 5Research Institute of Hospital Clínico San Carlos (IdISSC), Madrid, Spain
  6. 6Pneumology Department, Hospital Universitari Vall d'Hebron; Vall d'Hebron Institut de Recerca (VHIR), Vall d'Hebron Barcelona Hospital Campus, Barcelona, Spain
  7. 7Pneumology Department, Hospital Universitario Central de Asturias, Instituto de Investigacion Sanitaria del Principado de Asturias, Oviedo, Spain
  8. 8Pneumology Department, Hospital Universitario Nuestra Señora de La Candelaria, Santa Cruz de Tenerife, Spain
  9. 9Servicio de Neumología, Complejo Hospitalario Clínico-Universitario de Santiago, Santiago de Compostela, Spain
  10. 10Pneumology Section, Hospital Sierrallana-TresMares, Cantabria, Spain
  11. 11Servicio de Neumología, Hospital Clínico Universitario San Cecilio. Departamento de Medicina, Facultad de Medicina, Universidad de Granada, Granada, Spain
  12. 12Servicio de Neumología, Hospital Clínico Universitario, Instituto de Investigación INCLIVA, Valencia, Spain
  1. Corresponding Author: Marc Miravitlles (marcm{at}separ.es)
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Demographic and clinical characteristics of patients with alpha-1 antitrypsin deficiency genotypes PI*ZZ and PI*SZ in the Spanish registry of EARCO
María Torres-Durán, José Luis López-Campos, Juan Luis Rodríguez-Hermosa, Cristina Esquinas, Cristina Martínez-González, José María Hernández-Pérez, Carlota Rodríguez, Ana Bustamante, Francisco Casas-Maldonado, Miriam Barrecheguren, Cruz González, Marc Miravitlles
ERJ Open Research Jan 2022, 00213-2022; DOI: 10.1183/23120541.00213-2022

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Demographic and clinical characteristics of patients with alpha-1 antitrypsin deficiency genotypes PI*ZZ and PI*SZ in the Spanish registry of EARCO
María Torres-Durán, José Luis López-Campos, Juan Luis Rodríguez-Hermosa, Cristina Esquinas, Cristina Martínez-González, José María Hernández-Pérez, Carlota Rodríguez, Ana Bustamante, Francisco Casas-Maldonado, Miriam Barrecheguren, Cruz González, Marc Miravitlles
ERJ Open Research Jan 2022, 00213-2022; DOI: 10.1183/23120541.00213-2022
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