TY - JOUR T1 - Clinical characteristics of Immunoglobulin G4-positive interstitial pneumonia JF - ERJ Open Research JO - erjor DO - 10.1183/23120541.00317-2021 SP - 00317-2021 AU - Masamichi Komatsu AU - Hiroshi Yamamoto AU - Shoko Matsui AU - Yasuhiro Terasaki AU - Akira Hebisawa AU - Tae Iwasawa AU - Takeshi Johkoh AU - Tomohisa Baba AU - Atsushi Miyamoto AU - Tomohiro Handa AU - Keisuke Tomii AU - Yuko Waseda AU - Masashi Bando AU - Haruyuki Ishii AU - Yasunari Miyazaki AU - Akihiko Yoshizawa AU - Tamiko Takemura AU - Yoshinori Kawabata AU - Takashi Ogura A2 - , Y1 - 2021/01/01 UR - http://openres.ersjournals.com/content/early/2021/07/01/23120541.00317-2021.abstract N2 - Immunoglobulin (Ig) G4-related disease (IgG4-RD) is a systemic disease characterised by tumefactive lesions with abundant IgG4-positive plasma cells and elevated serum IgG4 concentrations [1–3]. We previously assessed IgG4-related respiratory disease (IgG4-RRD) with extrathoracic manifestations [4]. IgG4-RRD develops through the lymphatic routes in the lungs and responds well to corticosteroid therapy with a benign prognosis [4–6]. However, whether interstitial pneumonia (IP) with IgG4-positive plasma cell infiltration in the lungs without the extrathoracic lesions of IgG4-RD could be considered a type of IgG4-RRD is controversial.FootnotesThis manuscript has recently been accepted for publication in the ERJ Open Research. It is published here in its accepted form prior to copyediting and typesetting by our production team. After these production processes are complete and the authors have approved the resulting proofs, the article will move to the latest issue of the ERJOR online. Please open or download the PDF to view this article.Conflict of interest: Dr. Komatsu has nothing to disclose.Conflict of interest: Dr. Yamamoto has nothing to disclose.Conflict of interest: Dr. Matsui has nothing to disclose.Conflict of interest: Dr. Terasaki has nothing to disclose.Conflict of interest: Dr. Hebisawa has nothing to disclose.Conflict of interest: Dr. Iwasawa has nothing to disclose.Conflict of interest: Dr. Johkoh has nothing to disclose.Conflict of interest: Dr. Baba has nothing to disclose.Conflict of interest: Dr. Miyamoto has nothing to disclose.Conflict of interest: Dr. Handa has nothing to disclose.Conflict of interest: Dr. Tomii has nothing to disclose.Conflict of interest: Dr. Waseda has nothing to disclose.Conflict of interest: Dr. Bando has nothing to disclose.Conflict of interest: Dr. Ishii has nothing to disclose.Conflict of interest: Dr. Miyazaki has nothing to disclose.Conflict of interest: Dr. Yoshizawa has nothing to disclose.Conflict of interest: Dr. Takemura has nothing to disclose.Conflict of interest: Dr. Kawabata has nothing to disclose.Conflict of interest: Dr. Ogura has nothing to disclose. ER -