TABLE 1

Demographics, pulmonary function and bronchoalveolar lavage (BAL) cell count differential

Subjects10
Age years69.0 (63.7–76.0)
Male8 (80)
Smoking status
 Current0
 Ex5 (50)
 Never5 (50)
Pack-years (smokers)20 (10–30)
Clinical
 Biopsy done4 (40)
 PASP elevated6 (60)
 PAP mmHg36.8 (33.2–40.7)
N-acetyl cysteine treatment4 (40)
Pulmonary function
 FVC % pred73.5 (68.2–84.2)
 TLC % pred71.0 (60.0–77.0)
DLCO % pred47.5 (39.5–56.5)
 6MWT m420 (287–490)
BAL
 BAL cells obtained ×10619.2 (13.8–31.9)
 Macrophages %78.0 (69.0–91.2)
 Lymphocytes %5.0 (3.0–9.3)
 Neutrophils %9.0 (3.5–24.3)
 Eosinophils %0.75 (0–2.25)

Data are presented as n, median (interquartile range) or n (%). PASP: pulmonary artery systolic pressure; PAP: pulmonary arterial pressure; FVC: forced vital capacity; TLC: total lung capacity; DLCO: diffusing capacity of the lung for carbon monoxide; 6MWT: 6-min walk test.