Survival data
| All patients# | No or moderate BD¶ | Severe BD+ | |||||||
| NIV | No NIV | p-value | NIV | No NIV | p-value | NIV | No NIV | p-value | |
| Patients | 120 | 20 | 105 | 14 | 15 | 6 | |||
| Survival from ALS onset months | 43.00 (38.13–47.86) | 28.00 (21.40–34.57) | 0.001 | 43.00 (39.01–46.98) | 33.00 (26.64–39.35) | 0.002 | 40.00 (29.64–50.35) | 16.00 (5.19–26.80) | 0.002 |
| Survival from NIV months | 18.50 (12.62–24.38) | 3.00 (0.82–5.18) | 0.001 | 20.00 (13.71–26.28) | 3.00 (0.55–5.44) | 0.0001 | 13.00 (9.49–16.50) | 3.00 (0.85–5.14) | 0.001 |
Data are presented as mean (95% CI) unless otherwise stated. NIV: noninvasive ventilation; BD: bulbar dysfunction; ALS: amyotrophic lateral sclerosis. #: n=140; ¶: n=119; +: n=21.