TABLE 1

Subject characteristics

Underlying disease
 Infantile cerebral palsy8/20 (40)
 Congenital myopathy4/20 (20)
 Spinal muscular atrophy3/20 (15)
 Duchenne muscular dystrophy2/20 (10)
 Neuronal ceroid lipofuscinosis2/20 (10)
 Tracheomalacia1/20 (5)
Sex
 Female14/20 (70)
 Male6/20 (30)
Age years12.1±10.1 (1–37)
Tracheostomy9/20 (45)
 Infantile cerebral palsy3/8 (37.5)
 Congenital myopathy3/4 (75)
 Spinal muscular atrophy1/3 (33)
 Duchenne muscular dystrophy2/2 (100)
Noninvasive ventilation5/20 (25)
 Infantile cerebral palsy2/8 (25)
 Spinal muscular atrophy2/3 (66)
 Tracheomalacia1/1 (100)
Mechanically assisted cough15/20 (75)
 Infantile cerebral palsy4/8 (50)
 Congenital myopathy4/4 (100)
 Spinal muscular atrophy3/3 (100)
 Duchenne muscular dystrophy2/2 (100)
 Neuronal ceroid lipofuscinosis2/2 (100)

Data are presented as n/N (%) or mean±sd (range).