TABLE 5

Characteristics of patients with clinical follow-up data

Symptom changeImprovedWorsenedStable
Patients7 (20)1 (3)27 (77)
History of an obstructive lung disease4 (57)1 (100)11 (41)
PFT pattern
 Normal0 (0)0 (0)2 (7)
 Obstructive4 (57)1 (100)15 (56)
 Restrictive1 (14)0 (0)3 (11)
 Mixed0 (0)0 (0)1 (4)
 Nonspecific2 (29)0 (0)6 (22)
Positive bronchodilator response1 (14)1 (100)7 (26)
Constrictive bronchiolitis on biopsy3 (43)1 (100)11 (41)
Treatment given
 Observation1 (14)0 (0)7 (26)
 Inhaled β2-agonist5 (71)1 (100)9 (33)
 Inhaled antimuscarinic2 (29)0 (0)6 (22)
 ICS4 (57)0 (0)10 (37)
 Octreotide4 (57)0 (0)10 (37)

Data are presented as n (%). PFT: pulmonary function test; ICS: inhaled corticosteroid.