Fine–Gray univariable and multivariable competing risks models demonstrating prognostic factors for survival in patients with idiopathic pleuroparenchymal fibroelastosis (IPPFE) with usual interstitial pneumonia (UIP) (n=64)
Variable | Univariate | Multivariate | ||
SHR (95% CI) | p-value | SHR (95% CI) | p-value | |
Age | 1.000 (0.945–1.058) | 0.991 | ||
Female sex | 1.659 (0.753–3.651) | 0.209 | ||
BMI | 0.757 (0.632–0.907) | 0.003 | 0.806 (0.659–0.987) | 0.037 |
Ever-smokers | 0.754 (0.350–1.625) | 0.472 | ||
mMRC score | 0.996 (0.687–1.445) | 0.985 | ||
SpO2 <90% | 1.284 (0.601–2.742) | 0.518 | ||
FVC % predicted | 0.955 (0.929–0.982) | 0.001 | 0.971 (0.946–0.995) | 0.019 |
Prednisolone use | 0.502 (0.223–1.132) | 0.097 | 0.228 (0.072–0.727) | 0.012 |
Pneumothorax | 3.029 (1.366–6.714) | 0.006 |
SHR: subdistribution hazard ratio; BMI: body mass index; mMRC: modified Medical Research Council; SpO2: peripheral oxygen saturation; FVC: forced vital capacity.