TABLE 3

Fine–Gray univariable and multivariable competing risks models demonstrating prognostic factors for survival in patients with idiopathic pleuroparenchymal fibroelastosis (IPPFE) with usual interstitial pneumonia (UIP) (n=64)

VariableUnivariateMultivariate
SHR (95% CI)p-valueSHR (95% CI)p-value
Age1.000 (0.945–1.058)0.991
Female sex1.659 (0.753–3.651)0.209
BMI0.757 (0.632–0.907)0.0030.806 (0.659–0.987)0.037
Ever-smokers0.754 (0.350–1.625)0.472
mMRC score0.996 (0.687–1.445)0.985
SpO2 <90%1.284 (0.601–2.742)0.518
FVC % predicted0.955 (0.929–0.982)0.0010.971 (0.946–0.995)0.019
Prednisolone use0.502 (0.223–1.132)0.0970.228 (0.072–0.727)0.012
Pneumothorax3.029 (1.366–6.714)0.006

SHR: subdistribution hazard ratio; BMI: body mass index; mMRC: modified Medical Research Council; SpO2: peripheral oxygen saturation; FVC: forced vital capacity.