Comparison of causes of death between idiopathic pleuroparenchymal fibroelastosis (IPPFE) with usual interstitial pneumonia (UIP) and typical idiopathic pulmonary fibrosis (IPF)
| Variable | IPPFE with UIP | Typical IPF | p-value |
| Subjects n | 64 | 195 | |
| Lung cancer | 0 (0%) | 6 (3.0%) | 0.341 |
| Pneumonia | 12 (18.7%) | 16 (8.2%) | 0.034 |
| Acute exacerbation | 9 (14.0%) | 32 (16.4%) | 0.843 |
| Chronic deterioration | 20 (31.2%) | 15 (7.6%) | <0.0001 |
| Others | 3 (4.6%) | 11 (5.6%) | 1.000 |
| Unknown | 4 (6.2%) | 2 (1.0%) | 0.034 |
Data are presented as n (%) unless otherwise stated.