TABLE 1

Characteristics of the studied population

Patients299
Age years7.2±5.7
Male (n=298)162 (54.4)
Age at diagnosis months11.7±24.9
Diagnosis circumstances
 Neonatal screening (n=298)151 (50.7)
 Meconium ileus48 (16.0)
 Symptoms110 (37.0)
CFTR genotype
 ΔF508/ΔF508148 (49.5)
 ΔF508/other110 (36.7)
 Other41 (13.7)
History of microbiological status
 Haemophilus influenzae176 (59.1)
 Pseudomonas aeruginosa136 (45.6)
  Frequency of detection
   Only once64 (47.1)
   Intermittent51 (37.5)
   Chronic21 (15.4)
Staphylococcus aureus243 (81.5)
  Frequency of detection
   Only once31 (13.0)
   Intermittent104 (43.5)
   Chronic103 (43.1)
Clinical status at visit
 Exacerbations54 (18.1)
 Routine control244 (81.9)
Under antibiotic at visit119 (39.8)
 Azithromycin51 (43.2)
 Antibiotic targeting H. influenzae10 (8.5)
 Antibiotic targeting P. aeruginosa58 (28.8)
 Antibiotic targeting S. aureus34 (49.2)

Data are presented as n, mean±sd or n (%). CFTR: cystic fibrosis transmembrane conductance regulator.