Patients | 299 |
Age years | 7.2±5.7 |
Male (n=298) | 162 (54.4) |
Age at diagnosis months | 11.7±24.9 |
Diagnosis circumstances | |
Neonatal screening (n=298) | 151 (50.7) |
Meconium ileus | 48 (16.0) |
Symptoms | 110 (37.0) |
CFTR genotype | |
ΔF508/ΔF508 | 148 (49.5) |
ΔF508/other | 110 (36.7) |
Other | 41 (13.7) |
History of microbiological status | |
Haemophilus influenzae | 176 (59.1) |
Pseudomonas aeruginosa | 136 (45.6) |
Frequency of detection | |
Only once | 64 (47.1) |
Intermittent | 51 (37.5) |
Chronic | 21 (15.4) |
Staphylococcus aureus | 243 (81.5) |
Frequency of detection | |
Only once | 31 (13.0) |
Intermittent | 104 (43.5) |
Chronic | 103 (43.1) |
Clinical status at visit | |
Exacerbations | 54 (18.1) |
Routine control | 244 (81.9) |
Under antibiotic at visit | 119 (39.8) |
Azithromycin | 51 (43.2) |
Antibiotic targeting H. influenzae | 10 (8.5) |
Antibiotic targeting P. aeruginosa | 58 (28.8) |
Antibiotic targeting S. aureus | 34 (49.2) |
Data are presented as n, mean±sd or n (%). CFTR: cystic fibrosis transmembrane conductance regulator.