Ratings of factors influencing responder decision on individual need for follow-up at a cystic fibrosis (CF) specialist centre (n=54 responses)
| Would not contribute | Contributes somewhat | Major determinant | Total (weighted) | |
| Burkholderia cenocepacia complex sputum positive | 2 (3.7) | 13 (24.07) | 39 (72.22)# | 136.5 |
| Confirmed exocrine pancreatic insufficiency | 1 (1.85) | 15 (27.78) | 38 (70.37)# | 136.5 |
| Frequent pulmonary exacerbations | 3 (5.56) | 14 (25.93) | 37 (68.52)# | 132 |
| Pseudomonas aeruginosa sputum positive | 4 (7.41) | 19 (35.19) | 31 (57.41)# | 121.5 |
| Worse lung function at presentation | 5 (9.26) | 19 (35.19) | 30 (55.56)# | 118.5 |
| Recurrent pancreatitis | 3 (5.56) | 28 (51.85) | 23 (42.59) | 111 |
| Nutritional status/BMI | 5 (9.26) | 29 (53.7) | 20 (37.04) | 103.5 |
| NTM sputum positive | 7 (12.96) | 26 (48.15) | 21 (38.89) | 102 |
| Lung function relative to age at presentation | 10 (18.52) | 25 (46.3) | 19 (35.19) | 94.5 |
| MRSA sputum positive | 11 (20.37) | 26 (48.15) | 17 (31.48) | 90 |
| Other bacterial sputum positivity¶ | 10 (18.52) | 29 (53.7) | 15 (27.78) | 88.5 |
| Younger age at presentation | 12 (22.22) | 29 (53.7) | 13 (24.07) | 82.5 |
| Diagnosis of ABPA | 11 (20.37) | 33 (61.11) | 10 (18.52) | 79.5 |
| Confirmed diagnosis of diabetes | 17 (31.48) | 28 (51.85) | 9 (16.67) | 69 |
| Already attending a pulmonary specialist | 23 (42.59) | 27 (50) | 4 (7.41) | 52.5 |
Data are presented as n (%), unless otherwise stated. Total score calculated on a basis of 0, 1.5 and 3 points allocated for each count of “Would not contribute”, “Contributes somewhat” and “Major determinant”, respectively. BMI: body mass index; NTM: nontuberculous mycobacteria; MRSA: methicillin-resistant Staphylococcus aureus; ABPA: allergic bronchopulmonary aspergillosis. #: response with ≥50% selection as “Major determinant” of need for follow-up at a specialist CF centre; ¶: Stenotrophomonas, Achromobacter and methicillin-sensitive S. aureus.