Original ArticleEosinophilic granulomatosis with polyangiitis (Churg–Strauss) (EGPA) Consensus Task Force recommendations for evaluation and management
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Abbreviations
AAV
ANCA-associated vasculitides
ACR
American College of Rheumatology
ANCAs
antineutrophil cytoplasm antibodies
BVAS
Birmingham Vasculitis Activity Score
CRP
C-reactive protein
DVT
deep-vein thrombosis
ENT
ear, nose & throat
EGPA
eosinophilic granulomatosis with polyangiitis (Churg–Strauss)
ELISA
enzyme-linked immunosorbent assay
EULAR
European League Against Rheumatism
FFS
Five-Factor Score
GI
gastrointestinal
HE
hypereosinophilia
HES
hypereosinophilic syndromes
IL
interleukin
IV
intravenous
IVIg
IV immunoglobulins
LRA
leukotriene-receptor antagonists
MPO
myeloperoxidase
PR3
proteinase-3
SNV
systemic necrotizing vasculitis
VTEs
venous thromboembolic events
Keywords
Churg–Strauss syndrome
Anti-neutrophil cytoplasm antibody-associated vasculitis
Eosinophilia
Asthma
Recommendations
Eosinophilic granulomatosis with polyangiitis
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Copyright © 2015 European Federation of Internal Medicine. Published by Elsevier B.V.